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Epithelioid Hemangioendothelioma of the Infundibular–Hypothalamic
Region: Case Report and Literature Review
Abderrahmane Hamlat, Carlos Casallo-Quilliano, Stephan
Saikali, Thierry Lesimple, Gilles Brassier
Department
of Neurosurgery (A.H.), Department of Pathology (S.S.), Department of
Neurosurgery (G.B.), CHRU Pontchaillou, Rennes, France; Department of
Neurosurgery, Military Hospital, Lima, Peru (C.C.-Q.); Department of Medical
oncology, Centre Eugčne Marquis, Rennes, France (T.L.).
Epithelioid hemangioendothelioma (EHE) is an uncommon vascular
neoplasm.
Its intracranial occurrence is rare, and the literature review revealed only 23
cases (14 adults and 9 children).
To our knowledge, this is the first case of EHE arising in the infundibular–hypothalamic
region.
A 53-year-old man presented with headaches and loss of libido.
Magnetic resonance imaging revealed a supra-sellar mass, which homogeneously
absorbed the contrast agent.
A trans-sphenoidal craniotomy and a biopsy were performed.
Adjuvant radiotherapy was administered due to intolerance to interferon.
Epithelioid hemangioendothelioma is a hemorrhagic tumor.
Total resection is mandatory where possible, otherwise radiotherapy seems
necessary.
The prognosis of intracranial location has not yet been well defined, despite
the favorable outcome noted in the majority of cases.
Keywords: epithelioid hemangioendothelioma, hydrocephalus, infundibular–hypothalamic
neoplasm, interferon, radiotherapy, review
Copyright
©
2004 Kluwer Academic Publishers.
All rights reserved
Source: http://journals.kluweronline.com/article.asp?PIPS=5267135
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